Maffucci's syndrome complicated by intracranial chondrosarcoma: two new illustrative cases.

نویسندگان

  • Leandro Infantini Dini
  • Gustavo Rassier Isolan
  • Glauco Andre Saraiva
  • Simone Afonso Dini
  • Pasquale Gallo
چکیده

Maffucci's syndrome is a rare congenital condition, sometimes misdiagnosed as Ollier's disease, characterized by multiple enchondromas combined with hemangiomas and phlebectasia. Coexisting primary malignancies have been described sporadically. We report two cases of Maffucci's syndrome associated with cranial base chondrosarcoma, emphasizing pathophysiological features and the challenging management of intracranial chondrosarcomas. To the best of our knowledge, only twelve similar cases have been reported in the literature.

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عنوان ژورنال:
  • Arquivos de neuro-psiquiatria

دوره 65 3B  شماره 

صفحات  -

تاریخ انتشار 2007